Class I pentalogy of Cantrell: a rare case report

Authors : Bayram Ali Dorum, Hilal Ozkan, Nilgun Koksal, Yasemin Denkboy Ongen

Pages : 83-86

Doi:10.18621/eurj.293251

View : 26 | Download : 10

Publication Date : 2017-03-04

Article Type : Other

Abstract :Pentalogy of Cantrell is characterized by the presence of five major congenital defects involving the abdominal wall, pericardium, diaphragm, lower sternum and various cardiac abnormalities. This rare syndrome was described by Cantrell in 1958 and it has poor prognosis. We report here a case of class I Cantrell syndrome and our aim is to share difficulties experienced and review the related literature.
Keywords : Cantrell syndrome, ectopia cordis, omphalocele, ventricular diverticulum