- ODÜ Tıp Dergisi
- Vol: 10 Issue: 2
- A Case of Adult-onset Still’s Disease Complicated with Macrophage Activation Syndrome and Diffuse Al...
A Case of Adult-onset Still’s Disease Complicated with Macrophage Activation Syndrome and Diffuse Alveolar Hemorrhage
Authors : Kezban Armagan, Özgül Soysal Gündüz
Pages : 105-110
Doi:10.56941/odutip.1293362
View : 15 | Download : 16
Publication Date : 2023-08-31
Article Type : Research Article
Abstract :Adult-onset Still’s Disease (AOSD) is a rare inflammatory disease of unknown etiology characterized by high fever, skin rash, arthritis, elevated ferritin and organ involvement. Macrophage Activation Syndrome (MAS) can be seen as a rare, potentially fatal complication in AOSD. Here, we presented a case who was diagnosed with MAS due to general condition disorder, increased ferritin and cytopenia while being followed up with the diagnosis of chronic articular form ESH, and then developed diffuse alveolar hemorrhage (DAH) after a short time. We aimed to draw attention to rare complications after AOSD with this case report that showed a dramatic response to corticosteroid and tocilizumab treatment.Keywords : Erişkin Still Hastalığı, Diffüz alveoler hemoraji, Makrofaj Aktivasyon Sendromu, tosilizumab